OH-FORGE-BIOLOGICS
19.3.2024 13:01:30 CET | Business Wire | Press release
Forge Biologics, a member of Ajinomoto Bio-Pharma Services and a leading manufacturer of genetic medicines, today announced that the Medicines and Healthcare Products Regulatory Agency (MHRA), the healthcare regulatory body of the United Kingdom (UK), granted Innovation Passport designation to the Company’s novel AAV gene therapy program, FBX-101, to enter the Innovative Licensing and Access Pathway (ILAP). FBX-101 was created for the treatment of patients with Krabbe disease, a rare neurodegenerative disease that is usually fatal in untreated patients by age two. The ILAP is intended to accelerate regulatory and market access interactions in the UK.
Maria Escolar, M.D., Forge’s Chief Medical Officer, will discuss the significance of achieving this regulatory designation and present a poster on updated data from REKLAIM, an early phase clinical trial for FBX-101, during the Advanced Therapies 2024 conference being held in London, March 19-20, 2024.
“Considering the rapid progression of Krabbe disease in young patients and the positive results we’ve observed in the REKLAIM trial, we are pleased to receive the Innovation Passport designation which will enable Forge to further accelerate the clinical development of FBX-101,” stated Dr. Escolar. “ILAP was created to provide access to tools to decrease the time to market and facilitate patient access to medicines in the UK for life-threatening or seriously debilitating conditions.”
The REKLAIM clinical trial is evaluating the safety and efficacy of FBX-101 in patients with infantile and late infantile Krabbe disease. Children assessed in REKLAIM have received intravenous FBX-101 in addition to the current standard of care, hematopoietic stem cell transplantation (HSCT). Clinical data demonstrate that FBX 101 has been well tolerated and has an excellent safety profile after the treatment of five patients. Results show improvements in motor function in all patients, the most meaningful clinical outcome for this disease.
FBX-101 has been granted Orphan Drug Designation and Priority Medicines (PRIME) designation by the European Medicines Agency (EMA), allowing Forge to advance and expedite the development of FBX-101 as the leading worldwide gene therapy for patients with Krabbe disease. In the US, the FDA has granted FBX-101 Fast Track Designation, Orphan Drug Designation, and Rare Pediatric Disease Designation.
ILAP is intended to accelerate regulatory and market access interactions in the UK for patient populations with significant need, leading to accelerated patient access to novel therapies. It also provides access to a range of UK development services and tools, including frequent MHRA interactions, accelerated Marketing Authorization Application (MAA) assessment, a Target Development Profile, expanded licensing routes, and more, creating a roadmap for advancement of therapies through regulatory approval.
Regulatory review by the MHRA through ILAP provides opportunities for further global acceptance of Forge’s manufacturing process and facility though additional reviews and inspections, including Compliance Readiness Inspections that provide custom and pragmatic supervisory and licensing inspections specific to the GMP guidelines. Through this designation Forge has expanded global regulatory experience to include interactions with the MHRA in the UK. This access to global health authority resources will enable an added level of assurance to clients utilizing Forge’s CDMO services with integrated regulatory support.
About Krabbe Disease
Krabbe disease is a rare neurodegenerative disease affecting about 1-2.5 in 100,000 people in the US. Krabbe disease is caused by autosomal recessive mutations in the galactocerebrosidase (GALC) gene, an enzyme responsible for the breakdown of certain types of sphingolipids, such as psychosine. Without functional GALC, psychosine accumulates to toxic levels in cells, specifically in cells insulating the nerves in the brain and peripheral nervous system, causing rapid demyelination. Krabbe disease initially manifests in young patients as irritability, developmental delay, and progressive muscle weakness. Symptoms rapidly advance to difficulty swallowing, breathing, and regression of neurodevelopment followed by seizures, vision and hearing loss. Infantile Krabbe disease (0-12 months of age at onset) usually leads to death in untreated patients by two years of age. Late Infantile patients (12-36 months of age at onset) usually die by the age of six. The current standard of care, hematopoietic stem cell transplantation (HSCT), has been shown to stabilize cognitive decline and significantly improve long-term neurological outcomes. However, HSCT does not correct the peripheral neuropathy that is progressive as the patient grows, leading to loss of gross motor skills and eventually death.
About FBX-101
FBX-101 was developed to treat children with Krabbe disease. FBX-101 is an adeno-associated viral serotype rh10 (AAVrh10) gene therapy that is delivered intravenously after HSCT infusion. The vector delivers a functional copy of the GALC gene to cells in both the central and peripheral nervous system and has shown to functionally correct the central and peripheral neuropathy, improve myelination and gross motor function, and significantly prolong lifespan in animal models. This approach also has the potential to overcome some of the immunological safety challenges observed in traditional AAV gene therapies and extend the duration of gene transfer.
About the REKLAIM Trial
REKLAIM is a nonblinded, non-randomized, early phase dose escalation clinical trial currently enrolling children with asymptomatic infantile and symptomatic late infantile Krabbe disease to investigate the safety and efficacy of a single intravenous infusion of FBX-101 administered more than 21 days after HSCT, the current standard of care. Data from extensive natural history subjects will be used to compare as the control group. More information on the REKLAIM trial can be found online at https://www.clinicaltrials.gov/ct2/show/NCT05739643.
About Forge Biologics
Forge Biologics, a member of Ajinomoto Bio-Pharma Services, is a hybrid gene therapy contract manufacturing and clinical-stage therapeutics development company, enabling access to life-changing gene therapies by bringing them from concept to reality. Forge’s 200,000 square foot facility, the Hearth, is headquartered in Columbus, Ohio, and houses 20 custom-designed cGMP suites with 200,000L of manufacturing capacity. Forge’s end-to-end, scalable plasmid and AAV manufacturing services include research-grade manufacturing, process and analytical development, cGMP manufacturing, fill and finish, and integrated regulatory support to help accelerate the timelines of transformative medicines for patients with genetic diseases. To learn more, visit www.forgebiologics.com.
To view this piece of content from cts.businesswire.com, please give your consent at the top of this page.
View source version on businesswire.com: https://www.businesswire.com/news/home/20240319976189/en/
About Business Wire
Subscribe to releases from Business Wire
Subscribe to all the latest releases from Business Wire by registering your e-mail address below. You can unsubscribe at any time.
Latest releases from Business Wire
Samsung Unveils Industry's Fastest UFS 5.0 Solution for Next-Gen On-Device AI Applications23.6.2026 09:10:00 CEST | Press release
Samsung’s UFS 5.0 solution achieves industry's highest data transfer speed of 10.8GB/s, enabling faster storage and processing in mobile memoryEnhanced power efficiency and smaller package to provide optimal mobile AI experiences Samsung Electronics Co., Ltd., the world leader in advanced memory technology today announced that, for the first time in the industry, it has developed the industry's fastest Universal Flash Storage (UFS) 5.0 solution, which will help enable seamless and highly efficient AI services on future mobile devices. This press release features multimedia. View the full release here: https://www.businesswire.com/news/home/20260623632789/en/ Samsung Unveils Industry's Fastest UFS 5.0 Solution for Next-Gen On-Device AI Applications The milestone sets a new benchmark for the next-generation mobile memory market as the enhanced performance is expected to allow mobile device users with significantly reduced latency and faster response times when running large language mode
Varco Energy Selects NHOA Energy and IQA-Elecnor for 100MW Old Allen Road BESS23.6.2026 09:05:00 CEST | Press release
Varco Energy (Varco), a pioneering UK-based battery storage asset owner and operator backed by the Adaptogen Capital Battery Storage Fund, is pleased to announce it has signed supply contracts for its 100MW / 244MWh Old Allen Road Battery Energy Storage System (BESS) in West Yorkshire. Highlights: The Old Allen Road BESS adds 100MW to Varco’s portfolio of operational and in-construction projects, taking its operational BESS capacity to 350MW by the end of 2027, with a further 275MW in development. NHOA Energy, in consortium with IQA-Elecnor, will deliver the turnkey EPC project at Old Allen Road, with NHOA Energy supplying the BESS and IQA-Elecnor responsible for the associated balance of plant and interconnection works (33/275kV). GE Vernova has been contracted to provide the project 275kV High Voltage Transformer. The Old Allen Road BESS is a flagship project, designed to provide essential flexibility and grid-balancing services to the UK electricity system. Supply Contract Consortiu
Google and Energy Dome Advance Multi-Continent Energy Storage Buildout with First Bilateral Project in Ireland23.6.2026 09:00:00 CEST | Press release
The 23MW/200MWh CO2 Battery project marks the first bilateral commercial agreement between the companies, relieving grid congestion, promoting energy security and accelerating a 24/7 carbon-free energy solution in Ireland and beyond Today Energy Dome, a leading long-duration energy storage technology developer, and Google announced their first bilateral commercial contract for a 23MW / 200MWh CO2 Battery project located in County Offaly, Ireland. The project is part of a long-term partnership the companies announced last year to deploy Energy Dome’s CO2 Battery technology at scale and advance Google’s ambition to expand access to affordable, secure and 24/7 clean energy for grids globally. This announcement is on the back of a 19 MW/200 MWh project in Arizona announced this month by Energy Dome, Google, and the local utility SRP. This press release features multimedia. View the full release here: https://www.businesswire.com/news/home/20260623501211/en/ Rendering of Energy Dome's CO2 B
UNIQA Unifies Customer Risk Intelligence Across 14 Countries with SymphonyAI Financial Crime Compliance Platform23.6.2026 07:07:00 CEST | Press release
Austria's leading insurer implements centralized, insurance-specific AI for customer due diligence across Central and Eastern Europe UNIQA Insurance Group, one of Austria's and Europe's leading insurers, has selected the financial crime compliance platform from SymphonyAI, a global leader in Vertical AI, to unify customer due diligence (CDD) across its Central and Eastern European footprint. With operations spanning 14 countries and approximately 17 million customers, UNIQA brings one of the most complex compliance environments in the region to a single, centralized intelligence layer. Building for complexity, not around it UNIQA sought a CDD capability that matched the complexity of a pan-European insurer: one that could classify customers across risk categories consistently, keep pace with a shifting regulatory landscape across Central and Eastern Europe, and scale across diverse markets without requiring country-by-country customization. UNIQA selected SymphonyAI following a competi
Lenovo Recognized in the Gartner® Supply Chain Top 25 for 202623.6.2026 06:00:00 CEST | Press release
Lenovo has once again been ranked in the Gartner® Supply Chain Top 25 for 2026, achieving its highest-ever ranking at seventh globally. The Gartner Supply Chain Top 25 is a renowned annual ranking of the world’s superior supply chains. Now in its 22nd year, the Gartner Supply Chain Top 25 identifies, celebrates and profiles excellence in supply chain management. Supply chain teams use the Gartner Supply Chain Top 25 to benchmark performance, transform operations and lead in the future.Lenovo ranked eighth in 2025, 10th in 2024, and eighth in 2023. AI Builds Greater Supply Chain Resilience Global supply chains have faced unprecedented disruption over the past 12 months, driven by tariffs, component shortages, and geopolitical tensions. Lenovo’s strength amid these challenging circumstances has been its ability to build on its AI infrastructure behind its global supply chain, improving resilience, adaptability and execution at speed and scale. Over the past year, Lenovo has evolved its S
In our pressroom you can read all our latest releases, find our press contacts, images, documents and other relevant information about us.
Visit our pressroom
